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©2013 UpToDate ® Print Email Clinical and hereditary characteristics of amelogenesis imperfecta Type Clinical appearance Enamel thickness Radiographic appearance Inheritance Hypoplastic (type 1) Crown size varies from small to normal, small teeth may lack proximal contacts, color varies from normal to opaque white/yellow-brown Varies from thin and smooth to normal thickness with grooves, furrows, or pits Enamel has normal to slightly reduced contrast, thin Autosomal dominant, recessive, or X-linked Hypomaturation (type 2) Varies from creamy opaque to marked yellow or brown, surface of teeth soft and rough, dental sensitivity and open bite common Normal thickness with enamel that often chips and abrades easily Enamel has contrast similar to dentin, unerupted crowns have normal morphology Autosomal dominant, recessive, or X-linked Hypocalcified (type 3) Opaque white to yellow-brown, soft rough enamel surface, dental sensitivity and open bite common, heavy calculus formation common Normal thickness with enamel that often chips and abrades easily Enamel has contrast similar to or < dentin, unerupted crowns have normal morphology Autosomal dominant, recessive Hypomaturation/ hypoplasia/ taurodomism (type 4) White/yellow-brown mottled, teeth can appear small and lack proximal contact Reduced, hypomineralized areas and pits Enamel contrast normal to slightly > dentin, large pulp chambers Autosomal dominant Reproduced with permission from: Wright JT. Pediatr Clin North Am 2000; 47:986. Copyright 2000 W.B. Saunders Company.